Hailey-Hailey Disease - Key Clinical Features

(1) Vesicular lesions in flexures (neck, axillae, submammary region, groins and the perineum)

(2) Painful erosions (" rhagades ") in flexures

(3) Scaly erythematous plaques in flexures

(4) Itch

(5) Longitudinal white stripes of the nails

(6) Exacerbation by UVB irradiation, heat, friction, infection, sweating

(7) Malodorou plaques